|  | Diagnosis: Cor Triatriatum Cor Triatriatum: Facts Anomaly where the left atrium separated by a membrane or a fibromuscular bandIn pediatric patients associated with major congenital lesions including Tetrology of Fallot, double outlet right ventricle or coarctationUsually involves left atrium although occasionally may involve the right atrium0.1-0.4% of all infants with cardiac diseaseMost patients present in infancy but others may present in childhood or early adulthood
 Cor Triatriatum: Clinical Presentation AsymptomaticHeart murmurIncidental finding on imaging study
 SymptomaticExertional dyspneaHemoptysisAtrial fibrillation (palpitations)Systemic thromboembolism
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