Department of Radiology and Research Institute of Radiology, University of Ulsan College of Medicine, Asan Medical Center, Asanbyeongwon-Gil 86, Songpa-Gu, Seoul 138-736, Korea.
OBJECTIVE: The purpose of this essay is to illustrate a variety of atypical imaging manifestations of IgG4-related sclerosing disease in the abdomen and to correlate the imaging and pathologic findings. CONCLUSION: In rare instances, IgG4-related sclerosing disease manifests atypical features in various organs in the abdomen. It is important that radiologists be aware of the typical and atypical features of this disease to provide timely effective treatment.