Incomplete Double Aortic Arch with Atresia of the Distal Left Arch: Distinctive Imaging Appearance

Schlesinger AE, Krishnamurthy R, Sena LM, Guillerman RP, Chung T, DiBardino DJ, Fraser Jr. CD.

OBJECTIVE: We present 10 patients with double aortic arch with atresia of the distal left arch segment, a form of incomplete double aortic arch, and describe the distinct MRI and CT findings for this potentially symptomatic vascular ring.

CONCLUSION: Knowledge of the distinctive imaging appearance of this congenital arch anomaly can direct the radiologist to the correct preoperative diagnosis.