- Hemihypertrophy, partial gigantism - Vascular tumors and AVMs - Lipomas and fatty tumor proliferation - splenomegaly
Klippel-Trenaunay Syndrome: Facts
- Three key findings – Port wine stain – Abnormal vascular structures – Osseous and soft tissue hypertrophy
Kasabach-Merritt Syndrome: facts
- Consumptive thrombocytopenia and coagulopathy - Can lead to DIC - May have large hepatic or splenic hemangioma - Association with angiosarcoma and AVMs
Pulmonary Arteriovenous Malformations: Facts
- Congenital in origin - 60-90% of patients have hereditary hemorrhagic telangiectasia (aka Rendu- Osler-Weber syndrome)
